| CASE REPORT |
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| Year : 2008 | Volume
: 26
| Issue : 4 | Page : 177-181 |
Prosthetic rehabilitation of an adolescent with hypohidrotic ectodermal dysplasia with partial anodontia: Case report
S Kaul1, R Reddy2
1 MDS (Prosthodontics), ITS-CDSR, Ghaziabad, Uttar Pradesh, India
2 MDS (Pedodontics), Panineeya Mahavidyalaya Institute for Dental Science and Research Centre, Dilsukhnagar, Ranga Reddy District, Andhra Pradesh, India
Correspondence Address:
S Kaul
91, Block I, First Floor, Eros Garden, Charmwood Village, Surajkund, Faridabad, Haryana-121 009
India
DOI: 10.4103/0970-4388.44041 PMID: 19008629
Ectodermal dysplasia is a hereditary syndrome characterized by dysplasia of tissues of ectodermal origin (hair, skin, nails, and teeth) and occasionally, dysplasia of mesodermally derived tissues. The triad of nail dystrophy (onychodysplasia), alopecia, or hypotrichosis (scanty, fine, light hair on the scalp and eyebrows) and palmoplantar hypohidrosis is usually accompanied by lack of sweat glands and partial or complete absence of primary and permanent dentition. Hypohidrotic ectodermal dysplasia usually has an X-linked inheritance and affects only males severely, while female heterozygotes show only minor defects. The clinical management of children with ectodermal dysplasia provides a unique opportunity for cooperative effort between the pedodontist and the prosthodontist. The following case report discusses the management of a young boy with hypohidrotic ectodermal dysplasia. Removable prostheses were employed in the treatment. The aim was to rehabilitate the adolescent prosthodontically and boost him psychologically.
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