Journal of Indian Society of Pedodontics and Preventive Dentistry
Journal of Indian Society of Pedodontics and Preventive Dentistry
                                                   Official journal of the Indian Society of Pedodontics and Preventive Dentistry                           
Year : 2008  |  Volume : 26  |  Issue : 5  |  Page : 23--25

Pyknodysostosis: Oral findings and differential diagnosis


LF Soares1, I.P.R Souza1, AS Cardoso1, L Pomarico2 
1 Department of Oral Diagnosis and Oral Pathology, School of Dentistry, Federal University of Rio De Janeiro, Rio de Janeiro, RJ, Brazil
2 Department of Pediatric Dentistry, School of Dentistry, Federal University of Rio De Janeiro, Rio de Janeiro, RJ, Brazil

Correspondence Address:
L F Soares
Rua Visconde de PirajŠ, 4 /306, Ipanema, Rio de Janeiro 22410-000, RJ,
Brazil

Pyknodysostosis is a rare, genetic, autosomal recessive condition characterized by short stature, generalized bone sclerosis, and oral manifestations such as maxillary atresia and an increase of the mandibular angle. The main purpose of this article was to report a case of pyknodysostosis, describing the characteristic orofacial findings of the disease and discussing the differential diagnosis.


How to cite this article:
Soares L F, Souza I, Cardoso A S, Pomarico L. Pyknodysostosis: Oral findings and differential diagnosis.J Indian Soc Pedod Prev Dent 2008;26:23-25


How to cite this URL:
Soares L F, Souza I, Cardoso A S, Pomarico L. Pyknodysostosis: Oral findings and differential diagnosis. J Indian Soc Pedod Prev Dent [serial online] 2008 [cited 2019 Dec 11 ];26:23-25
Available from: http://www.jisppd.com/article.asp?issn=0970-4388;year=2008;volume=26;issue=5;spage=23;epage=25;aulast=Soares;type=0