Journal of Indian Society of Pedodontics and Preventive Dentistry
Journal of Indian Society of Pedodontics and Preventive Dentistry
                                                   Official journal of the Indian Society of Pedodontics and Preventive Dentistry                           
Year : 2008  |  Volume : 26  |  Issue : 7  |  Page : 118--120

Griscelli syndrome: A case report of Reye«SQ»s syndrome and atopic dermatitis history


Z Kirzioglu, AC Altun 
 Suleyman Demirel University, Faculty of Dentistry, Department of Pediatric Dentistry Isparta, Turkey

Correspondence Address:
A C Altun
Suleyman Demirel Universitesi Pedodonti AD. Cunur/Isparta
Turkey

Griscelli syndrome (GS) is a rare autosomal recessive disorder that results in pigmentary dilution of the skin and the hair (silver hair), with the presence of large clumps of pigment in hair shafts, and an accumulation of melanosomes in melanocytes. Sixty cases of GS have been reported in the literature, but we could find no description of its oro-dental symptoms. Reye«SQ»s syndrome (RS) is characterized by acute noninflammatory encephalopathy and renal and hepatic failure, while atopic dermatitis (AD) is a skin disorder with an immunologic basis. The aim of this paper is to describe the oro-dental and physical findings in a girl who had been diagnosed with GS at 3.5 years of age; she also had AD as well as a history of RS at infancy. We discuss the possible relationship between the three syndromes.


How to cite this article:
Kirzioglu Z, Altun A C. Griscelli syndrome: A case report of Reye's syndrome and atopic dermatitis history.J Indian Soc Pedod Prev Dent 2008;26:118-120


How to cite this URL:
Kirzioglu Z, Altun A C. Griscelli syndrome: A case report of Reye's syndrome and atopic dermatitis history. J Indian Soc Pedod Prev Dent [serial online] 2008 [cited 2020 Sep 20 ];26:118-120
Available from: http://www.jisppd.com/article.asp?issn=0970-4388;year=2008;volume=26;issue=7;spage=118;epage=120;aulast=Kirzioglu;type=0