Journal of Indian Society of Pedodontics and Preventive Dentistry
Journal of Indian Society of Pedodontics and Preventive Dentistry
                                                   Official journal of the Indian Society of Pedodontics and Preventive Dentistry                           
Year : 2011  |  Volume : 29  |  Issue : 1  |  Page : 62--67

Oral findings in a child with lipoid proteinosis: A case report and review


S Mainali, R Nayak, S Gaur 
 Department of Pedodontics and Preventive Dentistry, MCODS - affiliated to Manipal University, Manipal, India

Correspondence Address:
S Mainali
Department of Pedodontics and Preventive Dentistry, MCODS, Manipal - 576 104
India

Lipoid proteinosis, a very rare autosomal recessive genodermatosis, results in hyaline material deposition in the skin and mucous membrane of various organs leading to multisystem involvement. A case report of a 12-year-old female child is presented here who showed classic features of the disease with generalized thickening, hardening, and scarring of the skin and vocal cord infiltration causing voice changes. The patient also had numerous oral mucosal and dental findings. The knowledge of the clinical features of the disease may help the oral health professional in rendering the appropriate treatment in order to improve the quality of life deteriorated by the disease.


How to cite this article:
Mainali S, Nayak R, Gaur S. Oral findings in a child with lipoid proteinosis: A case report and review.J Indian Soc Pedod Prev Dent 2011;29:62-67


How to cite this URL:
Mainali S, Nayak R, Gaur S. Oral findings in a child with lipoid proteinosis: A case report and review. J Indian Soc Pedod Prev Dent [serial online] 2011 [cited 2019 Aug 25 ];29:62-67
Available from: http://www.jisppd.com/article.asp?issn=0970-4388;year=2011;volume=29;issue=1;spage=62;epage=67;aulast=Mainali;type=0