CASE REPORT |
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Year : 2007 | Volume
: 25
| Issue : 1 | Page : 43-45 |
Clinical and intraoral findings of a patient with tricho-rhino-phalangeal syndrome type I
S Karacay1, I Saygun2, Y Tunca3, N Imirzalioglu3, G Guvenc4
1 Department of Orthodontics, Gulhane Military Medical Academy, Ankara, Turkey 2 Department of Periodontology, Gulhane Military Medical Academy, Ankara, Turkey 3 Department of Genetics, Gulhane Military Medical Academy, Ankara, Turkey 4 Department of Pedodontics, Gulhane Military Medical Academy, Ankara, Turkey
Correspondence Address:
S Karacay Gulhane Military Medical Academy, Department of Orthodontics, 06018, Etlik-Ankara Turkey
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0970-4388.31990
Tricho-rhino-phalangeal syndrome (TRPS) is a rare and an autosomal dominant disorder having the following characteristics: slowly growing sparse hair, medially thick, and laterally thin eyebrows, bulbous tip of the nose, long flat philtrum and thin upper lip with vermilion border, protruding ears, cone-shaped epiphyses and swelling.
Our report intends to introduce TRPS to the dental literature and to present oral, clinical, and radiological data of a patient with TRPS. A rare association of supernumerary teeth was also diagnosed and one of them was extracted as it impeded on the eruption path of left premolar tooth.
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