| CASE REPORT |
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| Year : 2016 | Volume
: 34
| Issue : 2 | Page : 180-184 |
Gorham's disease of mandible - a rare case presentation in pediatric patient
Santanu Mukhopadhyay1, Abira Chattopadhyay2, Raja Bhattacharya3, Ushapati Roy4
1 Department of Pedodontics and Preventive Dentistry, Dr. R Ahmed Dental College and Hospital, Kolkata, West Bengal, India
2 Department of Oral and Maxillofacial Surgery, Burdwan Dental College and Hospital, Burdwan, West Bengal, India
3 Department of Pedodontics and Preventive Dentistry, Burdwan Dental College and Hospital, Burdwan, West Bengal, India
4 Department of Oral and Maxillofacial Pathology, Burdwan Dental College and Hospital, Burdwan, West Bengal, India
Correspondence Address:
Dr. Santanu Mukhopadhyay
Department of Pedodontics and Preventive Dentistry, Dr. R Ahmed Dental College and Hospital, Kolkata-700014, West Bengal
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/0970-4388.180450
Gorham's disease or vanishing bone disease is a rare, progressive musculoskeletal disorder characterized by resorption of bone matrix, and later replaced by fibrous connective tissue. The disease has no specific predilection for age, gender, or race. The most common sites of involvement are the shoulder and pelvic bones. To date, nearly 50 cases of Gorham's disease with maxillofacial involvement have been reported in the literature. The etiology of Gorham's disease is not known, clinical features are variable, and prognosis is generally good unless vital structures are involved. Due to the rarity of the condition, no definite treatment protocol exists for this disorder. Here, we described a pediatric case of Gorham's disease with mandibular involvement.
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