Journal of Indian Society of Pedodontics and Preventive Dentistry
Journal of Indian Society of Pedodontics and Preventive Dentistry
                                                   Official journal of the Indian Society of Pedodontics and Preventive Dentistry                           
Year : 2016  |  Volume : 34  |  Issue : 2  |  Page : 177--179

Darier俟Q製 disease - Oral, general and histopathological features in a 7 year old child


Sreedevi Dharman, Muthukrishnan Arvind 
 Department of Oral Medicine and Radiology, Saveetha Dental College and Hospital, Chennai, Tamil Nadu, India

Correspondence Address:
Dr. Sreedevi Dharman
Department of Oral Medicine and Radiology, Saveetha Dental College and Hospital, 162, Poonamallee High Road, Thiruverkadu, Chennai - 600 077, Tamil Nadu
India

Darier俟Q製 disease, also known as keratosis follicularis, is a rare autosomal dominant genodermatosis, manifesting clinically as hyperkeratotic, firm papule that predominates in the seborrheic areas and flexures with accompanying nail abnormalities. Heat, sweating, sunlight, and stress are exacerbating factors of the lesion. The oral lesions are asymptomatic and comprise multiple white papules in the buccal mucosa and hard palate, giving a cobblestone appearance, and it is characterized histologically by loss of desmosomal adhesion and abnormal keratinization resulting in mucocutaneous abnormalities. Pruritus, recurrent infections, and malodor can decrease the quality of life. We report a case of a 7-year-old boy with clinical and histological features of Darier俟Q製 disease.


How to cite this article:
Dharman S, Arvind M. Darier's disease - Oral, general and histopathological features in a 7 year old child.J Indian Soc Pedod Prev Dent 2016;34:177-179


How to cite this URL:
Dharman S, Arvind M. Darier's disease - Oral, general and histopathological features in a 7 year old child. J Indian Soc Pedod Prev Dent [serial online] 2016 [cited 2021 Oct 17 ];34:177-179
Available from: https://www.jisppd.com/article.asp?issn=0970-4388;year=2016;volume=34;issue=2;spage=177;epage=179;aulast=Dharman;type=0